A case of Barber-Say syndrome in a male Japanese newborn

نویسندگان

  • Kenichi Suga
  • Miki Shono
  • Aya Goji
  • Sato Matsuura
  • Miki Inoue
  • Masami Kawahito
  • Michiyo Kinoshita
  • Misa Takeda
  • Kazuhiro Mori
چکیده

KEY CLINICAL MESSAGE We reported a case of Barber-Say syndrome (BSS) in a Japanese newborn. Distinctive features of BSS were found; macrostomia, gingival dysplasia, cup-shaped low-set ears, wrinkling redundant skin, and hypertrichosis. Fundus showed subretinal drusenoid deposits, a novel finding of BSS. Genetic analysis is underway using next-generation genome sequencing and microarray analysis.

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عنوان ژورنال:

دوره 2  شماره 

صفحات  -

تاریخ انتشار 2014